Spinocerebellar Ataxias
Spinocerebellar Ataxias
Explore linked clinical trials. Standard reference: MESH:M002033738 results · Page 1 of 2
Clinical trials
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| Trial | Conditions | Status | Phase | Updated | More info | NCT ID |
|---|---|---|---|---|---|---|
| Multi-Modal Digital Monitoring of Disease Symptoms in Spinocerebellar Ataxia | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder | Not yet recruiting | Not stated | 2026-10-01 | NCT07851376 | |
| Rare Disease Registry Database for Movement Disorders in Southern Anhui Province | Congenital Abnormalities, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, central nervous system malformation, cerebellar ataxia, cerebellar disorder, hereditary disease, hereditary motor and sensory neuropathy, hereditary spastic paraplegia, inherited neurodegenerative disorder, motor neuron disorder, nervous system disorder, neurodegenerative disease, neuromuscular disease, peripheral nervous system disorder, polyneuropathy, spinal cord disorder | Active, not recruiting | Not stated | 2026-09-24 | NCT07838883 | |
| The Pancreas Interception Center (PIC) for Early Detection, Prevention, and Novel Therapeutics | Chronic Disease, Colorectal Neoplasms, Hereditary Nonpolyposis, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Cronkhite-Canada syndrome, Cysts, DNA repair disease, Digestive System Diseases, Digestive System Neoplasms, Disease Attributes, Dyskinesias, Familial Atypical Multiple Mole-Melanoma, Hyperpigmentation, Lynch syndrome, Melanosis, Neoplasms by Histologic Type, Neoplasms by Site, Neurologic Manifestations, Nutritional and Metabolic Diseases, Pancreatic Cyst, Pathologic Processes, Pathological Conditions, Signs and Symptoms, Peutz-Jeghers syndrome, Primary Immunodeficiency Diseases, Skin and Connective Tissue Diseases, Spinocerebellar Ataxias, atactic disorder, non-human animal, ataxia telangiectasia, brain disorder, cardiovascular disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, chronic pancreatitis, classic familial adenomatous polyposis, colonic disorder, colorectal neoplasm, digestive system disorder, digestive system neoplasm, hereditary disease, hereditary neoplastic syndrome, immune system disorder, inborn error of immunity, intestinal disorder, lentigo, melanocytic neoplasm, melanocytic nevus, melanoma, cutaneous malignant, susceptibility to, 2, metabolic disease, neoplasm, nervous system disorder, neurocutaneous syndrome, pancreas disorder, pancreatic ductal adenocarcinoma, pancreatitis, skin disorder, skin pigmentation disorder, telangiectasis, vascular disorder | Active, not recruiting | Not stated | 2026-09-15 | NCT05692596 | |
| Natural History of Spinocerebellar Ataxia Type 7 (SCA7) | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder | Active, not recruiting | Not stated | 2026-09-15 | NCT02741440 | |
| Pivotal Study of N-acetyl-L-leucine for CACNA1A | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, episodic ataxia type 2, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder, spinocerebellar ataxia type 6 | Recruiting | Phase 3 | 2026-09-08 | NCT07221292 | |
| Optimizing Parameters of Transcranial Temporal Interference Stimulation for Spinocerebellar Ataxia Type 3 | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Machado-Joseph disease, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder | Not yet recruiting | Not applicable | 2026-09-01 | NCT07743866 | |
| A Safety and Pharmacokinetics Trial of VO659 in SCA1, SCA3 and HD | Cognition Disorders, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Huntington disease, Machado-Joseph disease, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, basal ganglia disorder, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, choreatic disease, cognitive disorder, dementia, hereditary disease, inherited neurodegenerative disorder, movement disorder, nervous system disorder, neurodegenerative disease, psychiatric disorder, spinal cord disorder, spinocerebellar ataxia type 1 | Recruiting | Phase 1 / Phase 2 | 2026-08-19 | NCT05822908 | |
| Natural History Study of and Genetic Modifiers in Spinocerebellar Ataxias | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Machado-Joseph disease, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, Spinocerebellar ataxia 8, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder, spinocerebellar ataxia 7, spinocerebellar ataxia type 1, spinocerebellar ataxia type 10, spinocerebellar ataxia type 2, spinocerebellar ataxia type 6, spinocerebellar ataxia type 8 | Recruiting | Not stated | 2026-08-03 | NCT01060371 | |
| Interposed Nucleus aDBS for Ataxia | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder, spinocerebellar ataxia type 6 | Recruiting | Not applicable | 2026-07-20 | NCT07325487 | |
| Autosomal Dominant Spinocerebellar Ataxias and Social Cognition | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder | Recruiting | Not applicable | 2026-07-20 | NCT07099651 | |
| Biomarkers for Babies and Young Children With Ataxia Telangiectasia | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, DNA repair disease, Dyskinesias, Neurologic Manifestations, Nutritional and Metabolic Diseases, Primary Immunodeficiency Diseases, Spinocerebellar Ataxias, atactic disorder, non-human animal, ataxia telangiectasia, brain disorder, cardiovascular disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, immune system disorder, inborn error of immunity, metabolic disease, nervous system disorder, neurocutaneous syndrome, telangiectasis, vascular disorder | Not yet recruiting | Not stated | 2026-07-16 | NCT07709728 | |
| Deep Brain Stimulation for Spinocerebellar Ataxia | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder, spinocerebellar ataxia type 6 | Recruiting | Not applicable | 2026-07-13 | NCT07288437 | |
| Gait Analysis in Neurological Disease | Atypical Parkinson Disease, Cognition Disorders, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Gait Disorders, Neurologic, Gait, Frontal, Huntington disease, Neurologic Manifestations, Ocular Motility Disorders, Parkinson disease, Pathological Conditions, Signs and Symptoms, Signs and Symptoms, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, autonomic nervous system disorder, autosomal dominant Parkinson disease 1, basal ganglia disorder, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, choreatic disease, cognitive disorder, corticobasal degeneration disorder, cranial nerve neuropathy, dementia, eye disorder, hereditary disease, inherited neurodegenerative disorder, movement disorder, multiple system atrophy, nervous system disorder, neurodegenerative disease, ophthalmoplegia, palsy, parkinsonian disorder, primary dysautonomia, progressive supranuclear palsy, psychiatric disorder, spinal cord disorder, synucleinopathy, tauopathy | Active, not recruiting | Not stated | 2026-07-08 | NCT02994719 | |
| Study of ARO-ATXN2 Injection in Adults With Spinocerebellar Ataxia Type 2 | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder, spinocerebellar ataxia type 2 | Active, not recruiting | Phase 1 | 2026-06-29 | NCT06672445 | |
| Troriluzole in Adult Participants With Spinocerebellar Ataxia | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Machado-Joseph disease, Neurologic Manifestations, Pathological Conditions, Signs and Symptoms, Signs and Symptoms, Spinocerebellar Ataxias, Spinocerebellar Degenerations, Spinocerebellar ataxia 8, atactic disorder, non-human animal, brain disorder, cardiac arrest, cardiovascular disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, heart disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder, spinocerebellar ataxia 7, spinocerebellar ataxia type 1, spinocerebellar ataxia type 10, spinocerebellar ataxia type 2, spinocerebellar ataxia type 6, spinocerebellar ataxia type 8 | Active, not recruiting | Phase 3 | 2026-06-24 | NCT03701399 | |
| Real-World Data Study of Troriluzole-Treated Patients With Spinocerebellar Ataxia (SCA) Compared to a Matched Natural History Control | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder | Active, not recruiting | Not stated | 2026-06-09 | NCT06529146 | |
| Safety and Efficacy of Mutation-targeted Precision Genetic Therapy for Ataxia-Telangiectasia (A-T) | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, DNA repair disease, Dyskinesias, Neurologic Manifestations, Nutritional and Metabolic Diseases, Primary Immunodeficiency Diseases, Spinocerebellar Ataxias, atactic disorder, non-human animal, ataxia telangiectasia, brain disorder, cardiovascular disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, immune system disorder, inborn error of immunity, metabolic disease, nervous system disorder, neurocutaneous syndrome, telangiectasis, vascular disorder | Recruiting | Phase 1 / Phase 2 | 2026-05-28 | NCT07215416 | |
| Umbilical Cord Mesenchymal Stem Cells Therapy (19#iSCLife®-SA) for Patients With Spinocerebellar Ataxia | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Machado-Joseph disease, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder, spinocerebellar ataxia type 1, spinocerebellar ataxia type 2, spinocerebellar ataxia type 6 | Not yet recruiting | Phase 2 | 2026-04-23 | NCT03378414 | |
| Investigating the Genetic and Phenotypic Presentation of Ataxia and Nucleotide Repeat Diseases | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Pathological Conditions, Signs and Symptoms, Signs and Symptoms, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder | Active, not recruiting | Not stated | 2026-03-24 | NCT04529252 | |
| Wearable Gait Sensors | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder | Active, not recruiting | Not stated | 2026-02-05 | NCT06628934 | |
| An Phase Ib/II Clinical Trial of TCC1727 Combination Therapy in Advanced Solid Tumors | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, DNA repair disease, Digestive System Diseases, Digestive System Neoplasms, Dyskinesias, Female Urogenital Diseases, Female Urogenital Diseases and Pregnancy Complications, Genital Diseases, Neoplasms by Histologic Type, Neoplasms by Site, Neoplasms, Germ Cell and Embryonal, Neoplasms, Nerve Tissue, Neurologic Manifestations, Nutritional and Metabolic Diseases, Primary Immunodeficiency Diseases, Skin and Connective Tissue Diseases, Spinocerebellar Ataxias, Thoracic Neoplasms, Urogenital Diseases, Urogenital Neoplasms, atactic disorder, non-human animal, ataxia telangiectasia, brain disorder, bronchial neoplasm, bronchogenic carcinoma, cardiovascular disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, digestive system disorder, digestive system neoplasm, endometrium neoplasm, female reproductive system disorder, female reproductive system neoplasm, gastric neoplasm, hereditary disease, immune system disorder, inborn error of immunity, lung disorder, lung neoplasm, melanocytic neoplasm, melanoma, metabolic disease, neoplasm, nervous system disorder, neurocutaneous syndrome, neuroendocrine neoplasm, non-small cell lung carcinoma, primitive neuroectodermal tumor, respiratory system disorder, respiratory tract neoplasm, skin disorder, skin neoplasm, stomach disorder, telangiectasis, uterine disorder, vascular disorder | Recruiting | Phase 1 / Phase 2 | 2026-01-28 | NCT07371663 | |
| Efficacy of tDCS in Degenerative Ataxia | Ataxias, Hereditary, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Pathological Conditions, Signs and Symptoms, Signs and Symptoms, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder | Active, not recruiting | Not applicable | 2025-11-26 | NCT07250321 | |
| Ophthalmological Disorders in Dominant Spinal-cerebellar Ataxias | Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Neurologic Manifestations, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder | Recruiting | Not applicable | 2025-11-20 | NCT07019558 | |
| Gait Analysis Parameter and Upper Limb Evaluation in Adult Patients With Neurological or Metabolic Pathology | Body Weight, Charcot-Marie-Tooth disease, Cognition Disorders, Congenital Abnormalities, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Huntington disease, Lambert-Eaton myasthenic syndrome, Muscular Disorders, Atrophic, Neoplasms by Site, Neurologic Manifestations, Nutritional and Metabolic Diseases, Ocular Motility Disorders, Overweight, Paraneoplastic Syndromes, Nervous System, Pathological Conditions, Signs and Symptoms, Signs and Symptoms, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, autoimmune disease, autoimmune disorder of the nervous system, basal ganglia disorder, brain disorder, central nervous system disorder, central nervous system malformation, cerebellar ataxia, cerebellar disorder, choreatic disease, cognitive disorder, cranial nerve neuropathy, dementia, eye disorder, facioscapulohumeral muscular dystrophy, hereditary disease, hereditary motor and sensory neuropathy, hereditary spastic paraplegia, immune system disorder, inherited neurodegenerative disorder, movement disorder, muscle tissue disorder, muscular dystrophy, musculoskeletal system disorder, myasthenia gravis, myotonic dystrophy, myotonic syndrome, neoplasm, nervous system disorder, neurodegenerative disease, neuromuscular disease, neuromuscular junction disease, nutritional disorder, obesity disorder, ophthalmoplegia, overnutrition, palsy, paraneoplastic syndrome, peripheral nervous system disorder, polyneuropathy, psychiatric disorder, spinal cord disorder, tauopathy | Recruiting | Not applicable | 2025-08-22 | NCT07136844 | |
| Structural Validity and Inter-rater Reliabitiliy of the Ataxia Trunk, Lower And Upper Extremity Scale (ATLAS) | Ataxia, Motor, Ataxias, Hereditary, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Dyskinesias, Gait Ataxia, Gait Disorders, Neurologic, Neurologic Manifestations, Pathological Conditions, Signs and Symptoms, Signs and Symptoms, Spinocerebellar Ataxias, Spinocerebellar Degenerations, atactic disorder, non-human animal, brain disorder, central nervous system disorder, cerebellar ataxia, cerebellar disorder, hereditary disease, inherited neurodegenerative disorder, nervous system disorder, neurodegenerative disease, spinal cord disorder | Not yet recruiting | Not stated | 2025-08-13 | NCT07079332 |