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TrialConditionsStatusPhaseUpdatedMore infoNCT ID
A Clinical Study of Sotatercept (MK-7962) in People With Pulmonary Arterial Hypertension (MK-7962-038)lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderActive, not recruitingPhase 32026-10-08NCT07218029
A Study of ROC-101 in Patients With Pulmonary Arterial Hypertension (PAH) and Pulmonary Hypertension Associated With Interstitial Lung Disease (ILD-PH) (ROCSTAR STUDY)Congenital Abnormalities, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, cardiovascular disorder, central nervous system malformation, hereditary disease, hereditary sensory and autonomic neuropathy, hypertensive disorder, inherited neurodegenerative disorder, interstitial lung disease, lung disorder, nervous system disorder, neurodegenerative disease, neuromuscular disease, peripheral nervous system disorder, polyneuropathy, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorder, vascular disorderRecruitingPhase 22026-10-08NCT07175038
Spironolactone for Pulmonary Arterial Hypertensionlung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderRecruitingPhase 22026-10-08NCT01712620
A Study of Sotatercept (MK-7962) in Japanese Children With Pulmonary Arterial Hypertension (PAH) (MK-7962-032)lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderRecruitingPhase 22026-10-06NCT07646860
Fibrotic Disease Activity in Cardiopulmonary Disorders Using 18F-Fibroblast Activation Protein Inhibitor (18F-FAPI-74) PET/CT ImagingLung Injury, acute lung injury, cardiovascular disorder, interstitial lung disease, lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderRecruitingPhase 32026-10-06NCT07613099
Outcome Study Assessing a 75 Milligrams (mg) Dose of Macitentan in Patients With Pulmonary Arterial Hypertensionlung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderActive, not recruitingPhase 32026-10-06NCT04273945
A Study Evaluating the Long-Term Efficacy and Safety of Ralinepag in Subjects With PAH Via an Open-Label ExtensionFamilial Primary Pulmonary Hypertension, Skin and Connective Tissue Diseases, cardiovascular disorder, connective tissue disorder, hypertensive disorder, lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorder, vascular disorderEnrolling by invitationPhase 32026-10-06NCT03683186
A Study of Inhaled Treprostinil (LIQ861) in Adults With Pulmonary Arterial Hypertension Transitioning From Oral Selexipaglung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderRecruitingPhase 42026-10-02NCT07759804
PAH-SDB: Sleep-Disordered Breathing and Outcomes in Pulmonary Arterial HypertensionApnea, Dyssomnias, Respiration Disorders, Sleep Disorders, Intrinsic, central sleep apnea syndrome, lung disorder, nervous system disorder, obstructive sleep apnea syndrome, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorder, sleep apnea syndrome, sleep-wake disorderRecruitingNot stated2026-10-01NCT07852403
Microbiota Transplant With Antibiotic Preconditioning and Fiber Supplementation in PAH.lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderActive, not recruitingPhase 12026-09-28NCT07751120
Study of REGN13335 in Adult Participants With Pulmonary Arterial Hypertension (PAH)cardiovascular disorder, hypertensive disorder, lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorder, vascular disorderRecruitingPhase 22026-09-25NCT07318597
A Study Providing Treatment Access in Participants With Pulmonary Hypertension Completing a Parent Study and Having no Other Optioncardiovascular disorder, hypertensive disorder, lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorder, vascular disorderRecruitingPhase 32026-09-25NCT05179876
A Clinical Study of to Confirm the Doses of Selexipag in Children With Pulmonary Arterial Hypertensionlung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderActive, not recruitingPhase 22026-09-25NCT03492177
Pulmonary Arterial Hypertension Improvement With Nutrition and Exercise (PHINE)Inflammation, Insulin Resistance, Nutritional and Metabolic Diseases, Pathologic Processes, Pathological Conditions, Signs and Symptoms, glucose metabolism disease, hyperinsulinism, lung disorder, metabolic disease, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderActive, not recruitingNot applicable2026-09-25NCT03288025
Hormonal, Metabolic, and Signaling Interactions in PAHFamilial Primary Pulmonary Hypertension, idiopathic pulmonary arterial hypertension, lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderRecruitingNot stated2026-09-25NCT01884051
Tele-Pulmonary Rehabilitation For Patients With Chronic Lung DiseasesChronic Disease, Disease Attributes, Pathologic Processes, Pathological Conditions, Signs and Symptoms, chronic obstructive pulmonary disease, interstitial lung disease, lung disorder, obstructive lung disease, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderRecruitingNot applicable2026-09-24NCT07666841
Withdrawal of Prostacyclin Pathway Therapy in Patients With Pulmonary Arterial Hypertension Receiving Sotatercept (WATERLOO)lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderNot yet recruitingNot applicable2026-09-23NCT07700303
Riociguat in Children With Pulmonary Arterial Hypertension (PAH)cardiovascular disorder, hypertensive disorder, lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorder, vascular disorderActive, not recruitingPhase 32026-09-23NCT02562235
Multimodality RV Phenotyping for Risk Stratification and Short-Term Outcomes in Group 1 PAHcardiovascular disorder, hypertensive disorder, lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorder, vascular disorderActive, not recruitingNot stated2026-09-18NCT07667673
Global Utilization And Registry Database for Improved preservAtion of doNor LUNGsChronic Disease, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Digestive System Diseases, Disease Attributes, Fibrosis, Infant, Newborn, Diseases, Pathologic Processes, Pathological Conditions, Signs and Symptoms, chronic obstructive pulmonary disease, cystic fibrosis, hereditary disease, interstitial lung disease, lung disorder, obstructive lung disease, pancreas disorder, pulmonary arterial hypertension, pulmonary emphysema, pulmonary fibrosis, pulmonary hypertension, respiratory system disorderEnrolling by invitationNot stated2026-09-18NCT04930289
The Effect of Additive On-Demand Sildenafil vs. Dextrose Candy on Maximum Exercise Capacity in Pulmonary Arterial Hypertensionlung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderRecruitingPhase 2 / Phase 32026-09-17NCT07824674
A Study to Evaluate the Efficacy and Safety of Once Daily Treprostinil Palmitil Inhalation Powder (TPIP) in Participants With Pulmonary Arterial Hypertension (PAH)lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderRecruitingPhase 32026-09-16NCT07481981
A Multiple Dose Study to Investigate Safety, Tolerability and Pharmacokinetics of MN-08 Tabletslung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderNot yet recruitingPhase 12026-09-14NCT05660863
A Study of HS235 for Treatment of Pulmonary Arterial Hypertension (PAH) in Adultslung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorderRecruitingPhase 1 / Phase 22026-09-11NCT07143448
Exercise Performance on Ambient Air vs. Low-Flow Liquid Oxygen Therapy in Pulmonary Vascular Disease (PVD)cardiovascular disorder, hypertensive disorder, lung disorder, pulmonary arterial hypertension, pulmonary hypertension, respiratory system disorder, vascular disorderRecruitingNot applicable2026-09-09NCT07777445