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TrialConditionsStatusPhaseUpdatedMore infoNCT ID
ARTFL LEFFTDS Longitudinal Frontotemporal Lobar Degeneration (ALLFTD)Frontotemporal Lobar Degeneration, Neurologic Manifestations, Nutritional and Metabolic Diseases, Ocular Motility Disorders, Pathological Conditions, Signs and Symptoms, Signs and Symptoms, TDP-43 proteinopathy, amyotrophic lateral sclerosis, basal ganglia disorder, brain disorder, central nervous system disorder, cognitive disorder, corticobasal degeneration disorder, cranial nerve neuropathy, dementia, eye disorder, frontotemporal dementia, frontotemporal dementia with motor neuron disease, metabolic disease, motor neuron disorder, movement disorder, nervous system disorder, neurodegenerative disease, neuromuscular disease, ophthalmoplegia, palsy, proteostasis deficiencies, psychiatric disorder, spinal cord disorder, tauopathyRecruitingNot stated2026-10-07NCT04363684
Acamprosate in C9orf72 Hexanucleotide Repeat Expansion Amyotrophic Lateral Sclerosis (ACALS)Nutritional and Metabolic Diseases, TDP-43 proteinopathy, amyotrophic lateral sclerosis, central nervous system disorder, frontotemporal dementia with motor neuron disease, metabolic disease, motor neuron disorder, nervous system disorder, neurodegenerative disease, neuromuscular disease, proteostasis deficiencies, spinal cord disorderRecruitingPhase 12026-10-01NCT07204977
Effects of Probiotics in Amyotrophic Lateral Sclerosis-Frontotemporal Dementia Spectrum Disorder (ALS-FTDSD) PatientsNutritional and Metabolic Diseases, TDP-43 proteinopathy, amyotrophic lateral sclerosis, central nervous system disorder, frontotemporal dementia with motor neuron disease, metabolic disease, motor neuron disorder, nervous system disorder, neurodegenerative disease, neuromuscular disease, proteostasis deficiencies, spinal cord disorderRecruitingNot applicable2026-09-17NCT06051123
Neurofilament Surveillance Project (NSP)Frontotemporal Lobar Degeneration, Nutritional and Metabolic Diseases, TDP-43 proteinopathy, brain disorder, central nervous system disorder, cognitive disorder, dementia, frontotemporal dementia, frontotemporal dementia with motor neuron disease, metabolic disease, nervous system disorder, neurodegenerative disease, proteostasis deficiencies, psychiatric disorderActive, not recruitingNot stated2026-06-18NCT04516499
A Study of PBFT02 in Participants With FTD and Mutations in the Granulin Precursor (GRN) or C9ORF72 GenesFrontotemporal Lobar Degeneration, Nutritional and Metabolic Diseases, Pick disease, TDP-43 proteinopathy, brain disorder, central nervous system disorder, cognitive disorder, dementia, frontotemporal dementia, frontotemporal dementia with motor neuron disease, metabolic disease, nervous system disorder, neurodegenerative disease, proteostasis deficiencies, psychiatric disorderActive, not recruitingPhase 1 / Phase 22026-05-15NCT04747431
The Pre-symptomatic Familial Amyotrophic Lateral Sclerosis (Pre-fALS) StudyNutritional and Metabolic Diseases, TDP-43 proteinopathy, amyotrophic lateral sclerosis, central nervous system disorder, frontotemporal dementia with motor neuron disease, metabolic disease, motor neuron disorder, nervous system disorder, neurodegenerative disease, neuromuscular disease, proteostasis deficiencies, spinal cord disorderRecruitingNot stated2026-03-20NCT00317616
Amyotrophic Lateral Sclerosis (ALS) Families Projectamyotrophic lateral sclerosis, frontotemporal dementia with motor neuron diseaseRecruitingNot stated2026-01-07NCT03865420
Diagnosing Frontotemporal Lobar DegenerationFrontotemporal Lobar Degeneration, Neurobehavioral Manifestations, Neurologic Manifestations, Nutritional and Metabolic Diseases, Ocular Motility Disorders, Pathological Conditions, Signs and Symptoms, Signs and Symptoms, TDP-43 proteinopathy, aphasia, basal ganglia disorder, brain disorder, central nervous system disorder, cognitive disorder, communication disorder, corticobasal degeneration disorder, cranial nerve neuropathy, dementia, eye disorder, frontotemporal dementia, frontotemporal dementia and/or amyotrophic lateral sclerosis 1, frontotemporal dementia with motor neuron disease, language disorder, metabolic disease, movement disorder, nervous system disorder, neurodegenerative disease, ophthalmoplegia, palsy, primary progressive aphasia, progressive non-fluent aphasia, progressive supranuclear palsy, proteostasis deficiencies, psychiatric disorder, semantic dementia, speech disorder, tauopathyRecruitingNot stated2025-03-30NCT02964637