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TrialConditionsStatusPhaseUpdatedMore infoNCT ID
A Study to Investigate Efficacy, Safety and Tolerability of Barzolvolimab Versus Placebo in Adults With Cold Induced Urticaria and Symptomatic Dermographism Inadequately Controlled by H1-antihistamines (EMBARQ - ColdU and SD)Chronic Disease, Disease Attributes, Hypersensitivity, Immediate, Pathologic Processes, Pathological Conditions, Signs and Symptoms, Skin and Connective Tissue Diseases, chronic inducible urticaria, chronic urticaria, cold urticaria, familial dermatographia, immune system disorder, skin disorder, skin vascular disease, symptomatic dermographism, urticariaRecruitingPhase 32026-10-07NCT07266402
Study of Remibrutinib (LOU064) Efficacy and Safety and Exploration of Its Mechanism of Action in Participants With Chronic UrticariaChronic Disease, Disease Attributes, Hypersensitivity, Immediate, Pathologic Processes, Pathological Conditions, Signs and Symptoms, Skin and Connective Tissue Diseases, Urticaria, Solar, chronic inducible urticaria, chronic urticaria, cold urticaria, familial dermatographia, immune system disorder, photosensitivity disease, skin disorder, skin vascular disease, urticariaRecruitingPhase 22026-09-28NCT06865651
Natural History, Pathogenesis, and Outcome of Autoinflammatory Diseases (NOMID/CAPS, DIRA, CANDLE, SAVI, NLRC4-MAS, Still'S-like Diseases, and Other Undifferentiated Autoinflammatory Diseases)Chronic Disease, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Disease Attributes, Hypersensitivity, Immediate, Pathologic Processes, Pathological Conditions, Signs and Symptoms, STING-associated vasculopathy with onset in infancy, Skin and Connective Tissue Diseases, chronic inducible urticaria, chronic urticaria, cold urticaria, cryopyrin-associated periodic syndrome, hereditary disease, hereditary periodic fever syndrome, hereditary skin disorder, immune system disorder, skin disorder, skin vascular disease, sterile multifocal osteomyelitis with periostitis and pustulosis, urticariaRecruitingNot stated2026-09-22NCT02974595
A Phase 1 Study of GTX-B001 in Healthy Subjects and Patients With Chronic Inducible UrticariaChronic Disease, Disease Attributes, Hypersensitivity, Immediate, Pathologic Processes, Pathological Conditions, Signs and Symptoms, Skin and Connective Tissue Diseases, chronic inducible urticaria, chronic urticaria, cold urticaria, familial dermatographia, immune system disorder, skin disorder, skin vascular disease, symptomatic dermographism, urticariaRecruitingPhase 12026-09-09NCT07181369
A Study to Investigate Efficacy, Safety, and Tolerability of Remibrutinib Compared With Placebo in Adults With CINDU Inadequately Controlled by H1-antihistaminesChronic Disease, Disease Attributes, Hypersensitivity, Immediate, Pathologic Processes, Pathological Conditions, Signs and Symptoms, Skin and Connective Tissue Diseases, chronic inducible urticaria, chronic urticaria, cold urticaria, immune system disorder, skin disorder, skin vascular disease, urticariaActive, not recruitingPhase 32026-08-20NCT05976243
Study of BLU-808 in Chronic Inducible Urticaria (CIndU) and Chronic Spontaneous Urticaria (CSU)Chronic Disease, Chronic Spontaneous Urticaria, Disease Attributes, Hypersensitivity, Immediate, Pathologic Processes, Pathological Conditions, Signs and Symptoms, Skin and Connective Tissue Diseases, chronic inducible urticaria, chronic urticaria, cold urticaria, familial dermatographia, immune system disorder, skin disorder, skin vascular disease, urticariaActive, not recruitingPhase 22026-07-22NCT06931405
Repeat PET/CT Imaging in People With CAPS and Anakinra-Induced Amyloidosis Using an Amyloid-Reactive Peptide to Measure Changes in Organ-Specific Amyloid LoadChronic Disease, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Disease Attributes, Hypersensitivity, Immediate, Nutritional and Metabolic Diseases, Pathologic Processes, Pathological Conditions, Signs and Symptoms, Skin and Connective Tissue Diseases, amyloidosis, chronic inducible urticaria, chronic urticaria, cold urticaria, cryopyrin-associated periodic syndrome, hereditary disease, hereditary periodic fever syndrome, hereditary skin disorder, immune system disorder, metabolic disease, proteostasis deficiencies, skin disorder, skin vascular disease, urticariaRecruitingPhase 12026-05-19NCT06974877
Ilaris NIS in KoreaBlood Protein Disorders, Brain Diseases, Metabolic, Brain Diseases, Metabolic, Inborn, Chronic Disease, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Disease Attributes, Hemic and Lymphatic Diseases, Hypergammaglobulinemia, Hypersensitivity, Immediate, Nutritional and Metabolic Diseases, Pathologic Processes, Pathological Conditions, Signs and Symptoms, Peroxisomal Disorders, Skin and Connective Tissue Diseases, TNF receptor 1-associated periodic fever syndrome, arthritic joint disease, arthropathy, autoimmune disease, brain disorder, central nervous system disorder, chronic inducible urticaria, chronic urticaria, cold urticaria, connective tissue disorder, cryopyrin-associated periodic syndrome, hematologic disorder, hereditary disease, hereditary periodic fever syndrome, hereditary skin disorder, immune system disorder, immunoproliferative disorder, inborn errors of metabolism, juvenile idiopathic arthritis, metabolic disease, mevalonate kinase deficiency, musculoskeletal system disorder, nervous system disorder, rheumatic disorder, skin disorder, skin vascular disease, urticariaRecruitingNot stated2026-05-19NCT06838143
Circadian Rhythm Deregulation in Patients With CAPSChronic Disease, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Disease Attributes, Hypersensitivity, Immediate, Muckle-Wells syndrome, Pathologic Processes, Pathological Conditions, Signs and Symptoms, Skin and Connective Tissue Diseases, chronic inducible urticaria, chronic urticaria, cold urticaria, cryopyrin-associated periodic syndrome, familial cold autoinflammatory syndrome, hereditary disease, hereditary periodic fever syndrome, hereditary skin disorder, immune system disorder, skin disorder, skin vascular disease, urticariaRecruitingNot applicable2026-02-27NCT06544018
Are Mast Cells Involved in Autoinflammatory DiseasesChronic Disease, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Disease Attributes, Hypersensitivity, Immediate, Mast Cell Activation Disorders, Pathologic Processes, Pathological Conditions, Signs and Symptoms, Skin and Connective Tissue Diseases, TNF receptor 1-associated periodic fever syndrome, chronic inducible urticaria, chronic urticaria, cold urticaria, cryopyrin-associated periodic syndrome, familial Mediterranean fever, hereditary disease, hereditary periodic fever syndrome, hereditary skin disorder, immune system disorder, mast cell activation syndrome, mevalonic aciduria, skin disorder, skin vascular disease, urticariaNot yet recruitingNot stated2022-03-23NCT05292768